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christmas disease

/ˈkrɪsməs dɪˈziːz/

1 entry

phrase

/ˈkrɪsməs dɪˈziːz/C1formalmedical
  • ruРедкое генетическое нарушение свертываемости крови, также известное как гемофилия B, вызванное дефицитом фактора свертывания IX, приводящее к длительному кровотечению после травмы или операции.

A rare genetic bleeding disorder, also known as Hemophilia B, caused by a deficiency of clotting factor IX, resulting in prolonged bleeding after injury or surgery.

  1. Hemophilia BC1formal

    A genetic bleeding disorder caused by a deficiency of clotting factor IX, leading to prolonged bleeding after injury.

    ruГемофилия B

    • Christmas disease is less common than hemophilia A.
    • Patients with Christmas disease require regular factor IX infusions.
    • The condition was first identified in a patient named Stephen Christmas.